The Mount Sinai Journal of Medicine

 

Volume 72 Number 6
November 2005
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Grand Rounds

Pulmonary Artery Sarcoma Misdiagnosed as Chronic Thromboembolic Pulmonary Hypertension
360-364
Eric Widera, M.D.1, and Roxana Sulica, M.D.2

1Resident and 2Assistant Professor of Medicine, Cardiovascular Institute, Department of Medicine, Mount Sinai School of Medicine, New York, NY.

Address all correspondence to Roxana Sulica, M.D., Mount Sinai Pulmonary Hypertension Program, Box 1030, One East 100th Street, New York, NY 10029; email: Roxana.Sulica@mountsinai.org

Adapted from a Grand Rounds presentation to the Department of Medicine, Mount Sinai School of Medicine, New York, NY on June 29, 2004, and updated as of May 2005.

ABSTRACT

Pulmonary artery sarcomas are rare neoplasms of the pulmonary artery that are often confused with chronic thromboembolic disease, as both diseases have similar presentations. In patients with presumed chronic thromboembolic pulmonary hypertension, certain clinical and imaging characteristics may suggest the alternative diagnosis of pulmonary artery sarcoma. In this article we present a case of a man initially diagnosed with chronic thromboembolic pulmonary hypertension, but who was later found to have pulmonary artery sarcoma. We review the distinguishing characteristics of the two diseases and discuss possible treatment strategies.

KEY WORDS

Pulmonary artery sarcoma, chronic thromboembolic pulmonary hypertension, ventilation-perfusion scan, computed tomographic angiogram.
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